Gross right heart dilatation secondary to Ebstein's anomaly

Cardiac imaging is essential for the diagnosis and follow-up individuals with congenital heart disease (CHD). Currently echocardiography is the first-line investigation, although no single imaging technique is sufficient for complete evaluation of cardiac anatomy and physiology in these patients. Increasingly, adults with CHD are referred for cardiac magnetic resonance (CMR) imaging. Thehigh spatial resolution, functional assessment capabilities and excellent reproducibility of CMR make it a desirable investigation for CHD [1]. Ebstein’s anomaly is a rare (incidence ≈1 in 200 000 live births) congenital heart disorder characterized by malformations of the tricuspid valve (TV) and right ventricle (RV). The hallmark features are clearly demonstrated in this CMR study. They are: